Type IIIb congenital femoral deficiency. Case report
DOI:
https://doi.org/10.1016/j.rccot.2020.09.011Keywords:
deficiency, hypoplasia, rotational plasty, congenitalAbstract
We present the case of a 12-year-old male patient who presents a Postaxial Hypoplasia with a Congenital Femoral Deficiency type IIIb (Paley), characterized by absence of the proximal third of the femur also called Proximal Focal Femoral Deficiency and the presence of the distal third of the femur with a dysplastic knee with limited movement. Previous surgery in foot and ankle during early childhood with ankle ankylosis as a sequel. We performed a rotationoplasty with the Brown technique modified by Paley, knee pro-hip by iliofemoral fusion accompanied by a Syme distal amputation. The aim of this procedure was to achieve a functional limb by performing a neo-hip and a stump, that with an adequate prosthetic adaptation could achieve a gait pattern, similar to a supracondylar amputation or a disarticulation of the knee.
Evidence Level: IV
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References
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