Congenital fibrosarcoma of the knee. Case report
DOI:
https://doi.org/10.1016/j.rccot.2020.06.002Keywords:
congenital fibrosarcoma, knee, infant, tumorAbstract
Congenital fibrosarcoma is an unusual pathology, representing 3% of all childhood tumors. The purpose of the publication is to describe the clinical case of a patient with a congenital fibrosarcoma, successfully treated surgically without recurrences with good functional results.
We describe the clinical outcome of a 3-month-old of age with a mass in the left thigh by a congenital fibrosarcoma 10 cm, who underwent primary resection of the lesion with edges free of tumor compromise as the treatment of choice.
During follow-up, the patient did not present relapses with recovery of active and passive mobility arcs, with motor development according to age.
The congenital fibrosarcomas, are located mainly around the knee, and are infiltrating to adjacent tissues; management is surgical resection with tumor-free edges. Congenital Fibrosarcoma usually has better prognosis than adults sarcomas, but with recurrence rates up to 40% of the patients.
Evidence Level: IV
Downloads
References
Chung EB, Enzinger FM. Infantile fibrosarcoma. Cancer. 1976; 38:729-39. https://doi.org/c9k6gx
Erturka C, Yarımpapuc R, Akif M, Buyukbebecic O, Coskun M. A giant congenital fibrosarcoma of the leg. Orthop B. 2010;19:348-52. https://doi.org/10.1097/BPB.0b013e32833831fc
Ninane J, Gosseye S, Panteon E, Claus D, Rombouts JJ. Congenital fibromatosis Preoperative chemotherapy and conservative surgery. Cancer. 1986;58:1400-6. https://doi.org/bqhf95
Leal N, López JC, Díaz M, Ros Z, Pérez P, Tovar J. Fibrosarcoma congénito Implicaciones diagnóstico- terapéuticas. Cir Pediatr. 2000;13:156-8.
Gupta SS, Singh O, Sharma SS, Mathur RK. Congenital fibrosarcoma of the chest wall: report of a case. J Cutan Aesthet Surg. 2010;3:177-80. https://doi.org/10.4103/0974-2077.74497
Soule EH, Pritchard DJ. Fibrosarcoma in infants and children. A review of 110 cases. Cancer. 1977;40:1711-21. https://doi.org/ddpsrr
Blocker S, Koenig J, Ternberg J. Congenital fibrosarcoma. J Pediatr Surg. 1987;22:665-70. 8. Sachdev R, Singhal N, Mandal AK. Congenital fibrosarcoma of the upper extremity-a case report and review of literature. Indian J Pathol Microbiol. 2005;48:474-6. https://doi.org/10.1016/S0022-3468(87)80123-9
Sarreshtedar F, Mahzouni P, Besharati A, Naeimi A, Eftekhari A. A case report of Congenital Fibrosarcoma in an unusual location with multiple metastases. Am J Case Rep. 2008;9:342-5.
Vinnicombe SJ, Hall CM. Infantile fibrosarcoma: Radiological and clinical features. Skeletal Radiol. 1994;23:337-41. https://doi.org/c9k6gx
Martell JR, Busnardo MS, Barja RH. Congenital fibrosarcoma of the forearm. A case report. J Bone Joint Surg Am. 1986;68:620-3. https://doi.org/10.1007/BF02416988
Downloads
Published
How to Cite
Issue
Section
| Article metrics | |
|---|---|
| Abstract views | |
| Galley vies | |
| PDF Views | |
| HTML views | |
| Other views | |
